Abstract
Background: Short bowel syndrome (SBS) is an uncommon malabsorptive condition, most often caused by massive surgical resection of the small intestine, although it can also be congenital, especially in pediatric cases. SBS is associated with significant morbidity and mortality, reduced quality of life, and high healthcare costs.
Aim: To report a case of SBS in a newborn treated at the Pediatrics Service of Hospital Universitário São Francisco in Providência de Deus (HUSF), located in the city of Bragança Paulista, SP, Brazil.
Case Report: It was a newborn who was referred to the Neonatal Intensive Care Unit. Subsequently, the patient underwent an exploratory laparotomy with enterectomy, right partial colectomy, ileostomy, transverse colon burial using the Hartmann technique, appendectomy and cavity drainage. With severe malnutrition, the newborn received peripheral parenteral nutrition (PPN) until weight gain began (15g/day). After his nutritional status improved, he was discharged with outpatient follow-up.
Conclusion: Although it is associated with high morbidity and mortality, pediatric SBS can be circumvented with the help of surgical procedures and subsequent PN, as demonstrated in the case reported here, which had a favorable outcome.
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